Pediatrics

Congenital Heart Disease: Tetralogy of Fallot

Congenital Heart Disease: Tetralogy of Fallot

A cyanotic heart defect consisting of four anomalies: VSD, pulmonary stenosis, overriding aorta, and right ventricular hypertrophy.

Hypercyanotic Spell Management

  • Place infant in knee-to-chest position
  • Administer 100% oxygen by face mask
  • Provide morphine to reduce infundibular spasm
  • Remain calm to reduce child's distress

Post-op Care

  • Monitor for arrhythmias
  • Manage pain and maintain fluid balance
  • Encourage small, frequent feedings to conserve energy

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